Teaching NeuroImage: “Broomstick-Like” Appearance of Intracranial Arteries in ACTA2 Leukovasculopathy | Neurology
A 7-year-old boy presented with bilateral mydriasis. General examination was notable for prune belly. Neurologic examination showed loss of peripheral vision in the left eye. Brain MRI (Figure, A and B) revealed chronic white matter injury of bilateral posterior cerebral hemispheres raising concern for vasculopathy and a V-shaped corpus callosum. Brain MRA (Figure, C and D) showed irregular appearance of middle cerebral artery branches and distal anterior and posterior cerebral arteries. Given unusual
