Background/Purpose: VEXAS (Vacuoles, E1 enzyme, X-linked, Autoinflammatory, Somatic) syndrome, first described in 2020, is an autoinflammatory condition characterized by somatic mutations in the UBA1 gene. Predominantly affecting elderly males, VEXAS syndrome manifests with systemic inflammation and refractory hematologic abnormalities. Despite advancements in our understanding of this condition over the last 4 years, treatment recommendations for […]